Tay-Sachs disease is caused by a deficiency of __________ which results in an accumulation of ___________.
A)sphingomyelinase;sphingomyelin
B)ceramidase;ceramide
C)
α -galactosidase A;GM
1 ganglioside
D)lysosomal N-acetylhexosaminidase A;GM
2 ganglioside
E)
β -glucosidase;glucosylceramide